MALIGNANT MELANOMA
Overview
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Relatively uncommon, therefore all suspicious lesions should be referred under 2-week rule to local screening services
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A new mole appearing after the onset of puberty which is changing in shape, colour or size
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A long-standing mole which is changing in shape, colour or size
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Any mole which has three or more colours or has lost its symmetry
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A mole which is itching or bleeding
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Any new persistent skin lesion especially if growing, if pigmented or vascular in appearance, and if the diagnosis is not clear
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A new pigmented line in a nail especially where there is associated damage to the nail
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A lesion growing under a nail
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​Early recognition of melanoma presents the best opportunity for cure
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Risk factors:
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UV exposure​
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Age
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Previous melanoma
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Immunosuppression
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Family history
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Fitzpatrick skin type and hair colour
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Predisposing conditions
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Atypical mole syndrome​
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Dysplastic naevus​​
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Congenital naevus
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Xeroderma pigmentosum
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Lentigo maligna
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Histological subtypes
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Superficial spreading melanoma
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Most common​
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Long horizontal growth phase before vertical growth
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Flat junctional naevus, asymmetrical borders, colour variegation
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Nodular melanoma​
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Aggressive​
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Typically arises de novo in normal skin
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Dome shaped with sharp demarcation
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Lentigo maligna melanoma​​
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Least aggressive​
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Related to sub exposure
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Displays vertical growth phase as opposed to just radial growth phase of precursor lesion (lentigo maligna)
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Acral lentiginous melanoma​
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Usually on palms, soles of feet, subungual or sun-protected areas​
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Usually flat with irregular border and multiple colour shades
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Desmoplastic melanoma​
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Propensity for perineural invasion​
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High rate of regional lymph node spread
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Amelanotic melanoma​
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No pigment by light microscopy​
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Diagnosis by immunohistochemistry​
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Staging
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TNM staging in accordance to American Joint Committee on Cancer (AJCC) 8th edition
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Breslow thickness - tumour thickness in millimetres from stratum granulosum
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Ulceration of the primary tumour upstages the disease to the next T substage
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Mitotic rate ≥ 1 per squared mm is independently associated with worse disease-specific survival
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T-stage
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Tx - Primary tumour thickness cannot be assessed​
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T0 - No evidence of primary tumour
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Tis - Melanoma in situ
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T1
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T1a - <0.8mm without ulceration​
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T1b - <0.8mm with ulceration or 0.8-1.0 mm with or without ulceration
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T2
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T2a - >1.0-2.0mm​ without ulceration
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T2b - >1.0-2.0mm with ulceration
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T3​
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T3a - >2.0-4.0mm without ulceration​
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T3b - >2.0-4.0mm with ulceration
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T4​
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T4a - >4.0mm without ulceration​
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T4b - >4.0mm with ulceration
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N-stage​​
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Nx - Regional nodes not assessed​
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N0 - No regional metastases detected
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N1
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N1a - 1 clinically occult (detected by sentinel lymph node biopsy)​
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N1b - 1 clinically detected
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N1c - No regional lymph node disease, with presence of in-transit, satellite and/or microsatellite metastases
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N2​
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N2a - 2-3 clinically occult​
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N2b - 2-3 involved nodes, at least one of which was clinically detected
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N2c - 1 clinically occult or clinically detected, with presence of in-transit, satellite and/or microsatellite metastases
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N3​
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N3a - ​≥4 clinically occult​
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N3b - ≥4 involved nodes, at least one of which was clinically detected or the presence of any number of matted nodes
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N3c - ≥2 clinically occult or clinically detected and/or presence of any number of matted nodes, with presence of in-transit, satellite and/or microsatellite metastases
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M-stage
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M0 - No evidence of distant metastasis​
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M1 - Evidence of distant metastasis
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M1a
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M1a(0) - Distant metastasis to skin, soft tissue including muscle, and/ or nonregional lymph node​, LDH not elevated
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M1a(1) - Distant metastasis to skin, soft tissue including muscle, and/ or nonregional lymph node​, LDH elevated
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M1b
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M1b(0) - Distant metastasis to lung with or without M1a sites of disease​, LDH not elevated
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M1b(1) - Distant metastasis to lung with or without M1a sites of disease​, LDH elevated
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M1c​
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M1c(0) - ​Distant metastasis to non-CNS visceral sites with or without M1a or M1b sites of disease​, LDH not elevated
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M1c(1) - Distant metastasis to non-CNS visceral sites with or without M1a or M1b sites of disease​, LDH elevated
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M1d​
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M1d(0) - Distant metastasis to CNS with or without M1a, M1b or M1c sites of disease​, LDH not elevated
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M1d(1) - Distant metastasis to CNS with or without M1a, M1b or M1c sites of disease​, LDH elevated
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AJCC prognostic stage group​​
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0 - Tis N0 M0​
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IA - T1a-T1b N0 M0
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IB - T2a N0 M0
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IIA - T2b-T3a N0 M0
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IIB - T3b-T4a N0 M0
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IIC - T4b N0 M0
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IIIA - T1a/b-T2a N1a/N2a M0
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IIIB - T0 N1b/N1c M0, T1a/b-T2a N1b/c or N2b M0, or T2b/T3a N1a-N2b M0
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IIIC - T1a-T3a N2c N3a/b/c M0, T3b/T4a ≥N1 M0, or T4b N1a-N2c M0
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IV - Any T Any N M1
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Investigations
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Excision biopsy with 2mm margins with cuff of fat
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Pathological evaluate for Breslow thickness​, ulceration, mitotic rate, deep and peripheral margins, microsatellites
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Imaging​
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Stages I and II - CT, PET/CT, MRI generally not recommended​
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Stage III - CT chest/abdomen/pelvis, CT/MRI brain with or without PET/CT​
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Management
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Wide local excision (WLE) of primary tumour
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Reduce local recurrence
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Depth of excision to but not including next fascial layer
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Margins​​
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In situ - 5mm​ margin
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<1mm - 1cm​ margin
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≥1mm - 2cm margin
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Sentinel lymph node biopsy​​
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Staging procedure​, not therapeutic treatment
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Performed in conjunction with WLE of primary tumour
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Indicated for stage IB melanoma
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Lymph node dissection
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No role ​​for elective lymph node dissection in negative SLNB
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Therapeutic lymph node dissection in positive SLNB did not improve melanoma-specific survival (MSLT-II trial)
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Therapeutic lymph node dissection indicated in patients not suitable for immunotherapy, who cannot attend for follow-ups (usually for geographical reasons)
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Immunotherapy​
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Rapidly advancing adjuvant treatment option​
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Ipilimumab - monoclonal antibody directed to CTLA-4 receptor
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​Vemurafenib - BRAF kinase inhibitor​
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Imatinib - for tumours with c-KIT mutation
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